Hledali jste: Methyl-2-hydroxyisobutyrate

Katalogové číslo: (ACRO436180050)

Dodavatel: Thermo Scientific

Popis: Methyl (R)-(-)-3-hydroxyisobutyrate 98%

Měrná jednotka: 1 * 5 g

Bezpečnostní list Akce

Dodavatel: Apollo Scientific

Popis: Methyl-2-hydroxyisobutyrate 95%

Dodavatel: Apollo Scientific

Popis: Methyl (R)-(-)-3-hydroxyisobutyrate 97%

Dodavatel: Thermo Scientific

Popis: Appearance: Clear colorless Liquid

Bezpečnostní list

Dodavatel: Thermo Scientific

Popis: (S)-(+)-Methyl-3-hydroxy-2-methylpropionate ≥98%

Bezpečnostní list Certifikáty

Dodavatel: Merck

Popis: Methyl (R)-(-)-3-hydroxyisobutyrate, Sigma-Aldrich®

Dodavatel: Thermo Scientific

Popis: Ethyl-2-hydroxyisobutyrate ≥98%

Bezpečnostní list

Dodavatel: Thermo Scientific

Popis: 2-Hydroxyisobutyric acid 98%

Bezpečnostní list

Katalogové číslo: (APOSOR46219-25G)

Dodavatel: Apollo Scientific

Popis: Ethyl-2-hydroxyisobutyrate 98%

Měrná jednotka: 1 * 25 g

Akce

Dodavatel: Apollo Scientific

Popis: 2-Hydroxyisobutyric acid

Dodavatel: Thermo Scientific

Popis: 2-Hydroxyisobutyric acid, (max. 2% H₂O) 99% (dry weight)

Bezpečnostní list Certifikáty

Katalogové číslo: (BOSSBS-15483R-HRP)

Dodavatel: Bioss

Popis: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (BOSSBS-15483R-CY7)

Dodavatel: Bioss

Popis: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (BOSSBS-15483R-A647)

Dodavatel: Bioss

Popis: HIBADH is a 336 amino acid mitochondrial enzyme that catalyses the NAD+-dependent, reversible oxidisation of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7,0 and 10,0, with optimal activity between 8,8 and 9,0. It was previously hypothesised that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterised by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (BOSSBS-15483R)

Dodavatel: Bioss

Popis: HIBADH is a 336 amino acid mitochondrial enzyme that catalyzes the NAD+-dependent, reversible oxidization of 3-Hydroxyisobutyrate to methylmalonate semialdehyde, an intermediate of valine catabolism. The enzyme functions as a homodimer between a pH of 7.0 and 10.0, with optimal activity between 8.8 and 9.0. It was previously hypothesized that defects in the gene encoding HIBADH may be the cause of 3-Hydroxyisobutyric aciduria, a rare disorder that is characterized by a variety of clinical manifestations such as neurodevelopmental problems and dysmorphic features. However, it was shown that HIBADH activity was equal in patients with 3-Hydroxyisobutyric aciduria as compared with controls.

Měrná jednotka: 1 * 100 µl

Akce

Dodavatel: Apollo Scientific

Popis: (R)-3,3,3-Trifluoro-2-hydroxy-2-methylpropionic acid 97%