Hledali jste: DSG+(Disuccinimidyl+glutarate)

Katalogové číslo: (BOSSBS-0494R-CY5)

Dodavatel: Bioss

Popis: ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008].

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (BOSSBS-0494R-HRP)

Dodavatel: Bioss

Popis: ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric, lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008].

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (SPCMD2948-200LTBL)

Dodavatel: Spectrum Chemical

Popis: Dimethyl Glutarate is used in de-icing and anti-icing applications, construction and road applications, and release and binders agents.

Měrná jednotka: 1 * 200 L

Akce

Katalogové číslo: (BOSSBS-13312R)

Dodavatel: Bioss

Popis: GCDH is a 438 amino acid protein that localizes to the mitochondrial matrix and belongs to the acyl-CoA dehydrogenase family. Existing as a homotetramer, GCDH uses FAD as a cofactor to catalyze the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine and L-tryptophan metabolism. While GCDH exists as both a long and short isoform, only the long isoform is a functionally active protein. Defects in the gene encoding GCDH are the cause of glutaric acidemia type I (GA-I), an autosomal recessive disorder that is characterized by the accumulation of glutaconic acid and is associated with such symptoms as progressive dystonia and athetosis due to gliosis and neuronal loss in the basal ganglia.

Měrná jednotka: 1 * 100 µl

Akce

Katalogové číslo: (8.20604.0250)

Dodavatel: Merck

Popis: Glutaric anhydride for synthesis, Sigma-Aldrich®

Měrná jednotka: 1 * 250 g

Bezpečnostní list Akce

Katalogové číslo: (BOSSBS-13312R-HRP)

Dodavatel: Bioss

Popis: GCDH is a 438 amino acid protein that localizes to the mitochondrial matrix and belongs to the acyl-CoA dehydrogenase family. Existing as a homotetramer, GCDH uses FAD as a cofactor to catalyze the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine and L-tryptophan metabolism. While GCDH exists as both a long and short isoform, only the long isoform is a functionally active protein. Defects in the gene encoding GCDH are the cause of glutaric acidemia type I (GA-I), an autosomal recessive disorder that is characterized by the accumulation of glutaconic acid and is associated with such symptoms as progressive dystonia and athetosis due to gliosis and neuronal loss in the basal ganglia.

Měrná jednotka: 1 * 100 µl

Akce

Dodavatel: Merck

Popis: Methyl hydrogen glutarate, Sigma-Aldrich®

Dodavatel: Merck

Popis: Organic Standard, Glutaric acid-1,2,3,4-¹³C₄ sodium salt

Katalogové číslo: (89147-100MG)

Dodavatel: Merck

Popis: Organic Standard, Glutaric acid

Měrná jednotka: 1 * 100 mg

Akce

Dodavatel: Merck

Popis: Kyselina glutarová, Sigma-Aldrich®

Dodavatel: Merck

Popis: Glutaraldehyd 50% in aqueous solution, Sigma-Aldrich®

Dodavatel: Merck

Popis: Glutaraldehyd 50% in aqueous solution, Sigma-Aldrich®

Dodavatel: Merck

Popis: Glutardialdehyde is a fixing agent for specimens destined for morphological and enzyme histochemical analysis of samples of human origin.

Bezpečnostní list Certifikáty

Dodavatel: Merck

Popis: Glutaraldehyd 50% aqueous solution, Sigma-Aldrich®

Certifikáty

Dodavatel: Merck

Popis: Kyselina glutarová for synthesis, Sigma-Aldrich®

Bezpečnostní list

Katalogové číslo: (EHERC14034500)

Dodavatel: EHRENSTORFER

Popis: Kyselina glutarová

Měrná jednotka: 1 * 0,25 g

Akce